| Anaemia among females in child-bearing age: Relative contributions, effects and interactions of α- and β-thalassaemia. | Mettananda S, Suranjan M, Fernando R, Dias T, Mettananda C, Rodrigo R, Perera L, Gibbons R, Premawardhena A, Higgs D | PLoS ONE | 2018 |
| A structure-guided approach to ameliorate sickle cell disease. | Richter-Addo GB | Acta Crystallogr D Struct Biol | 2018 |
| Pediatric residents' perceived barriers to opioid use in sickle cell disease pain management. | Fearon A, Marsh A, Kim J, Treadwell M | Pediatr Blood Cancer | 2018 |
| Indwelling ports for prophylactic RBC exchanges in sickle cell patients: Comparison of bard and vortex ports. | Lawicki S, Craig-Owens L, Bream PR, Eichbaum Q | J Clin Apher | 2018 |
| Student perspectives on managing sickle cell disease at school. | Haridasa N, DeBaun MR, Sanger M, Mayo-Gamble TL | Pediatr Blood Cancer | 2018 |
| Hemoglobin oxidation-dependent reactions promote interactions with band 3 and oxidative changes in sickle cell-derived microparticles. | Jana S, Strader MB, Meng F, Hicks W, Kassa T, Tarandovskiy I, De Paoli S, Simak J, Heaven MR, Belcher JD, Vercellotti GM, Alayash AI | JCI Insight | 2018 |
| Sleep disorders and endothelial dysfunction in children with sickle cell anemia. | Ramos-Machado V, Ladeia AM, Dos Santos Teixeira R, da Anunciação Ferreira T, Terse-Ramos R | Sleep Med. | 2018 |
| Clinical Outcomes Associated With Sickle Cell Trait: A Systematic Review. | Naik RP, Smith-Whitley K, Hassell KL, Umeh NI, de Montalembert M, Sahota P, Haywood C, Jenkins J, Lloyd-Puryear MA, Joiner CH, Bonham VL, Kato GJ | Ann. Intern. Med. | 2018 |
| Denosumab in transfusion-dependent thalassemia osteoporosis: a randomized, placebo-controlled, double-blind phase 2b clinical trial. | Voskaridou E, Ntanasis-Stathopoulos I, Papaefstathiou A, Christoulas D, Dimopoulou M, Repa K, Papatheodorou A, Peppa M, Terpos E | Blood Adv | 2018 |
| Evaluation of continuous glucose monitoring system for detection of alterations in glucose homeostasis in pediatric patients with β-thalassemia major. | El-Samahy MH, Tantawy AAG, Adly AAM, Abdelmaksoud A, Ismail EAR, El-Din NYS | Pediatr Diabetes | 2018 |
| [Rapid preimplantation genetic diagnosis of -thalassemia SEA deletion with blastocyst cell whole genome amplification and short fragment Gap-PCR method]. | Xu H, Liu Y, Yan P, He Y, Qin J, Lou J, Zhou W | Nan Fang Yi Ke Da Xue Xue Bao | 2018 |
| CRISPR in personalized medicine: Industry perspectives in gene editing. | Hong A | Semin. Perinatol. | 2018 |
| Falsely high HbA value due to a novel α1-globin gene mutation: Hb shantou [α127(H10)Lys > Glu; HBA1: c.382 A > G]. | Xu A, Lei J, Li J, Chen W, Zhou Y, Zheng R, Ji L | Scand. J. Clin. Lab. Invest. | 2018 |
| Production and Transduction of a Human Recombinant β-Globin Chain into Proerythroid K-562 Cells To Replace Missing Endogenous β-Globin. | Papadopoulou LC, Ingendoh-Tsakmakidis A, Mpoutoureli CN, Tzikalou LD, Spyridou ED, Gavriilidis GI, Kaiafas GC, Ntaska AT, Vlachaki E, Panayotou G, Samiotaki M, Tsiftsoglou AS | Mol. Pharm. | 2018 |
| Effect of serum fibroblast growth factor receptor 2 and CAPS proteins on calcium status in β-thalassaemia major patients who are free from overt inflammation. | Al-Hakeim HK, Alhillawi ZH | Growth Factors | 2018 |
| Living Fully with Sickle Cell Disease. | Anim M | J Gen Intern Med | 2018 |
| Iron Chelation with Transdermal Deferoxamine Accelerates Healing of Murine Sickle Cell Ulcers. | Rodrigues M, Bonham CA, Minniti CP, Gupta K, Longaker MT, Gurtner GC | Adv Wound Care (New Rochelle) | 2018 |
| Bone Marrow Necrosis in Sickle Cell-Beta Thalassemia Patient Mimicking Thrombotic Thrombocytopenic Purpura. | Myers CF, Ipe TS | Ann. Clin. Lab. Sci. | 2018 |
| Green tea extract modulates oxidative tissue injury in beta-thalassemic mice by chelation of redox iron and inhibition of lipid peroxidation. | Koonyosying P, Kongkarnka S, Uthaipibull C, Svasti S, Fucharoen S, Srichairatanakool S | Biomed. Pharmacother. | 2018 |
| Rh E antigen in a multi-transfused patient with sickle cell disease. | Alves VM, Martins PRJ, De Vito FB, Castilho L, Moraes-Souza H | Hematol Transfus Cell Ther | 2018 |
| Primary Cutaneous Mucormycosis in a Beta-Thalassemia Patient. | Sepaskhah M, Moezzi I, Davarpanah MA, Sari Aslani F | Indian J Hematol Blood Transfus | 2018 |
| Ushering a New Era in the Management of Hepatitis C in Children with Hematological Disorders. | Sivasankaran M, Venkatadesikalu M, Mythili V, Sankaranarayanan S, Jayaraman D, Patel S, Swaminathan VV, Uppuluri R, Raj R | Indian J Hematol Blood Transfus | 2018 |
| HbE Level and Red Cell Parameters in Heterozygous HbE With and Without α-Thalassemia Trait. | Pornprasert S, Tookjai M, Punyamung M, Pongpunyayuen P | Indian J Hematol Blood Transfus | 2018 |
| Low IL-2 Expressing T Cells in Thalassemia Major Patients: Is It Immune Aging. | Pourgheysari B, Karimi L, Bagheri R, Kheiri S | Indian J Hematol Blood Transfus | 2018 |
| Zoledronic Acid for Treatment of Low Bone Mineral Density in Patients with Beta Thalassemia Major. | Naithani R, Seth T, Tandon N, Chandra J, Choudhry VP, Pati H, Saxena R | Indian J Hematol Blood Transfus | 2018 |
| Soluble receptor for advanced glycation end products as a vasculopathy biomarker in sickle cell disease. | Safwat NA, Kenny MA | Pediatr. Res. | 2018 |
| Prenatal diagnosis and management of fetal discordant alpha-thalassaemia in dichorionic diamniotic (DCDA) twins. | Panchalee T, Ruangvutilert P, Limsiri P, Sutcharitpongsa P | BMJ Case Rep | 2018 |
| Cerebral Vasoreactivity in Children with Sickle Cell Disease: A Transcranial Doppler Study. | Prakash K | J Stroke Cerebrovasc Dis | 2018 |
| Emerging Regulatory Role of Nrf2 in Iron, Heme, and Hemoglobin Metabolism in Physiology and Disease. | Kasai S, Mimura J, Ozaki T, Itoh K | Front Vet Sci | 2018 |
| Efficacy of Oral Acetaminophen and Intravenous Chlorpheniramine Maleate versus Placebo to Prevent Red Cell Transfusion Reactions in Children and Adolescent with Thalassemia: A Prospective, Randomized, Double-Blind Controlled Trial. | Rujkijyanont P, Monsereenusorn C, Manoonphol P, Traivaree C | Anemia | 2018 |
| Virtual reality as complementary pain therapy in hospitalized patients with sickle cell disease. | Agrawal AK, Robertson S, Litwin L, Tringale E, Treadwell M, Hoppe C, Marsh A | Pediatr Blood Cancer | 2018 |
| Hydroxyurea prevents onset and progression of albuminuria in children with sickle cell anemia. | Zahr RS, Hankins JS, Kang G, Li C, Wang WC, Lebensburger J, Estepp JH | Am. J. Hematol. | 2018 |
| Erythema ab igne in patients with sickle cell disease. | Samaan CB, Valentin MN, Jamison MO, Ellison K, Marathe KS, Norton SA, Kirkorian AY | Pediatr Hematol Oncol | 2018 |
| Striking dyserythropoiesis in sickle cell anemia following an aplastic crisis. | Austin A, Lund K, Bain BJ | Am. J. Hematol. | 2018 |
| Emerging Genetic Therapy for Sickle Cell Disease. | Orkin SH, Bauer DE | Annu. Rev. Med. | 2018 |
| Hemoglobinopathies in the Fetal Position. | Pasricha SR, Drakesmith H | N. Engl. J. Med. | 2018 |
| Sickle related events following cardiac catheterisation: risk implication for other invasive procedures. | Di Maggio R, Conrey A, Taylor TN, Lederman RJ, Rogers T, Nichols J, Bouges S, Minniti CP, Kato GJ, Shet AS, Hsieh MM | Br. J. Haematol. | 2018 |
| Hemoglobin F as a predictor of health-related quality of life in children with sickle cell anemia. | Boulassel MR, Al-Badi A, Elshinawy M, Al-Hinai J, Al-Saadoon M, Al-Qarni Z, Khan H, Qureshi RN, Wali Y | Qual Life Res | 2018 |
| Analysis of Gene Mutation Types of α- and β-Thalassemia in Fuzhou, Fujian Province in China. | Xu C, Liao B, Qi Y, Huangfu Z, Chen J, Chen Y | Hemoglobin | 2018 |
| Maternal sickle cell disease and twin pregnancy: a case series and review of the literature. | Cardosa D, Ridout A, Nanda S, Howard J, Robinson SE, Oteng-Ntim E | Hematology | 2018 |
| Risk of avascular necrosis of the femoral head in children with sickle cell disease on hydroxyurea: MRI evaluation. | Adekile AD, Gupta R, Al-Khayat A, Mohammed A, Atyani S, Thomas D | Pediatr Blood Cancer | 2018 |
| Human hemoglobin G-Makassar variant masquerading as sickle cell anemia. | Mohamad AS, Hamzah R, Selvaratnam V, Yegapan S, Sathar J | Hematol Rep | 2018 |
| Synergistic Protective Effect of Sickle Cell Trait and Blood Group-O on the Risk of Endemic Burkitt's Lymphoma. | Ahamed SG, Ibrahim UA, Kagu MB | Gulf J Oncolog | 2018 |
| Existence, triggers, and coping with chronic sorrow: a qualitative study of caretakers of children with sickle cell disease in a National Referral Hospital in Kampala, Uganda. | Olwit C, Mugaba M, Osingada CP, Nabirye RC | BMC Psychol | 2018 |
| Association between sickle cell disease and the oral health condition of children and adolescents. | Brandão CF, Oliveira VMB, Santos ARRM, da Silva TMM, Vilella VQC, Simas GGPP, Carvalho LRS, Carvalho RAC, Ladeia AMT | BMC Oral Health | 2018 |
| A Patient of Chronic Hepatitis C Complicated by Thalassemia Major and Chronic Osteomyelitis: A Therapeutic Challenge for a Clinician. | Sarkar R, Paul R, Roy D, Ghosh R, Sau TJ, Lahiri G, Ruia AV | J Assoc Physicians India | 2018 |
| Acceptability and Feasibility of a Disease-specific Patient Portal in Adolescents With Sickle Cell Disease. | Kidwell KM, Peugh J, Westcott E, Nwankwo C, Britto MT, Quinn CT, Crosby LE | J. Pediatr. Hematol. Oncol. | 2018 |
| Drugs for preventing red blood cell dehydration in people with sickle cell disease. | Nagalla S, Ballas SK | Cochrane Database Syst Rev | 2018 |
| Multicenter validation of the magnetic resonance T2* technique for quantification of pancreatic iron. | Meloni A, De Marchi D, Pistoia L, Grassedonio E, Peritore G, Preziosi P, Restaino G, Righi R, Riva A, Renne S, Schicchi N, Vallone A, Peluso A, Gerardi C, Positano V, Pepe A | Eur Radiol | 2018 |
| Sotatercept, a novel transforming growth factor beta ligand trap, improves anemia in beta-thalassemia: a phase 2, open-label, dose-finding study. | Cappellini MD, Porter J, Origa R, Forni GL, Voskaridou E, Galactéros F, Taher AT, Arlet JB, Ribeil JA, Garbowski M, Graziadei G, Brouzes C, Semeraro M, Laadem A, Miteva D, Zou J, Sung V, Zinger T, Attie KM, Hermine O | Haematologica | 2018 |
| The survival rate of patients with beta major thalassemia and thalassemia intermedia and its trend in recent years in Iran. | Ansarimoghaddam A, Adineh H, Mohammadi M, Zareban I, Maghsoudloo M | Epidemiol Health | 2018 |
| Newborn screening for sickle cell disease in Europe: recommendations from a Pan-European Consensus Conference. | Lobitz S, Telfer P, Cela E, Allaf B, Angastiniotis M, Backman Johansson C, Badens C, Bento C, Bouva MJ, Canatan D, Charlton M, Coppinger C, Daniel Y, de Montalembert M, Ducoroy P, Dulin E, Fingerhut R, Frömmel C, García-Morin M, Gulbis B, Holtkamp U, Inusa B, James J, Kleanthous M, Klein J, Kunz JB, Langabeer L, Lapouméroulie C, Marcao A, Marín Soria JL, McMahon C, Ohene-Frempong K, Périni JM, Piel FB, Russo G, Sainati L, Schmugge M, Streetly A, Tshilolo L, Turner C, Venturelli D, Vilarinho L, Yahyaoui R, Elion J, Colombatti R, | Br. J. Haematol. | 2018 |
| MRI multicentre prospective survey in thalassaemia major patients treated with deferasirox versus deferiprone and desferrioxamine. | Pepe A, Meloni A, Pistoia L, Cuccia L, Gamberini MR, Lisi R, D'Ascola DG, Rosso R, Allò M, Spasiano A, Restaino G, Righi R, Mangione M, Positano V, Ricchi P | Br. J. Haematol. | 2018 |
| Peripheral Neuropathy in Thalassemia Major. | Kaushik JS, Verma A, Sharma H, Bala K, Dabla S, Yadav A | Indian J Pediatr | 2018 |
| Elevated levels of platelet- and red cell-derived extracellular vesicles in transfusion-dependent β-thalassemia/HbE patients with pulmonary arterial hypertension. | Manakeng K, Prasertphol P, Phongpao K, Chuncharunee S, Tanyong D, Worawichawong S, Svasti S, Chaichompoo P | Ann. Hematol. | 2018 |
| Evaluation of Iron Overload Between Age Groups Using Magnetic Resonance Imaging and Its Correlation with Iron Profile in Transfusion-dependent Thalassemia. | Wahidiyat PA, Iskandar SD, Sekarsari D | Acta Med Indones | 2018 |
| The platelet NLRP3 inflammasome is upregulated in sickle cell disease via HMGB1/TLR4 and Bruton tyrosine kinase. | Vogel S, Arora T, Wang X, Mendelsohn L, Nichols J, Allen D, Shet AS, Combs CA, Quezado ZMN, Thein SL | Blood Adv | 2018 |
| [Sickle Cell Disease in Newborns in Germany: Analysis of the AOK Health Insurance Data]. | Pattloch D | Gesundheitswesen | 2018 |
| Pathophysiology of Sickle Cell Disease. | Sundd P, Gladwin MT, Novelli EM | Annu Rev Pathol | 2018 |
| [Acute chest syndrome in sickle cell disease]. | Bopp T, Stephan C, Samii K, Stirnemann J | Rev Med Suisse | 2018 |
| Increased Patient Activation Is Associated with Fewer Emergency Room Visits and Hospitalizations for Pain in Adults with Sickle Cell Disease. | Cronin RM, Dorner TL, Utrankar A, Allen W, Rodeghier M, Kassim AA, Jackson GP, DeBaun MR | Pain Med | 2018 |
| Hb Penang [β78(EF2)Leu→Pro, HBB: c.236T>C]: a Novel β-Globin Variant. | Hsu CH, Langdown J, Lynn R, Fisher C, Rose A, Proven M, Eglinton J, Besser MW | Hemoglobin | 2018 |
| Use of metformin in patients with sickle cell disease. | Han J, Saraf SL, Molokie RE, Gordeuk VR | Am. J. Hematol. | 2018 |
| Benzene metabolite 1,2,4-benzenetriol changes DNA methylation and histone acetylation of erythroid-specific genes in K562 cells. | Yu CH, Li Y, Zhao X, Yang SQ, Li L, Cui NX, Rong L, Yi ZC | Arch. Toxicol. | 2018 |
| Red blood cell mechanical sensitivity improves in patients with sickle cell disease undergoing chronic transfusion after prolonged, subhemolytic shear exposure. | Simmonds MJ, Suriany S, Ponce D, Detterich JA | Transfusion | 2018 |
| Promise of gene therapy to treat sickle cell disease. | Romero Z, DeWitt M, Walters MC | Expert Opin Biol Ther | 2018 |
| A novel BaEVRless-pseudotyped γ-globin lentiviral vector drives high and stable HbF expression and improves thalassemic erythropoiesis in vitro. | Drakopoulou E, Georgomanoli M, Lederer CW, Kleanthous M, Costa C, Bernadin O, Cosset FL, Voskaridou E, Verhoeyen E, Papanikolaou E, Anagnou NP | Hum. Gene Ther. | 2018 |
| Differential cerebral hemometabolic responses to blood transfusions in adults and children with sickle cell anemia. | Juttukonda MR, Lee CA, Patel NJ, Davis LT, Waddle SL, Gindville MC, Pruthi S, Kassim AA, DeBaun MR, Donahue MJ, Jordan LC | J Magn Reson Imaging | 2018 |
| Multiple Integrated Non-clinical Studies Predict the Safety of Lentivirus-Mediated Gene Therapy for β-Thalassemia. | Lidonnici MR, Paleari Y, Tiboni F, Mandelli G, Rossi C, Vezzoli M, Aprile A, Lederer CW, Ambrosi A, Chanut F, Sanvito F, Calabria A, Poletti V, Mavilio F, Montini E, Naldini L, Cristofori P, Ferrari G | Mol Ther Methods Clin Dev | 2018 |
| Conventional and advanced brain MR imaging in patients with sickle cell anemia. | Issar P, Nehra M, Singh G, Issar SK | Indian J Radiol Imaging | 2018 |
| Gender influences on the health of adolescents with sickle cell disease. | Barton-Gooden A, Grindley M, Knight-Madden J, Asnani M | Psychol Health Med | 2018 |
| Severe, non specific symptoms in non-typhoidal Salmonella infections in adult patients with sickle cell disease: a retrospective multicentre study. | Guery R, Habibi A, Arlet JB, Lionnet F, de Lastours V, Decousser JW, Mainardi JL, Razazi K, Baranes L, Bartolucci P, Godeau B, Galacteros F, Michel M, Mahevas M | Infect Dis (Lond) | 2018 |
| A Fatal Case of Necrotizing Pancreatitis in Sickle Cell Beta Thalassemia Zero. | Turnbull TL, Houston PM, Batalis NI | Am Surg | 2018 |
| Comparable Outcomes of Allogeneic Peripheral Blood versus Bone Marrow Hematopoietic Stem Cell Transplantation in Major Thalassemia: A Multivariate Long-Term Cohort Analysis. | Ghavamzadeh A, Kasaeian A, Rostami T, Kiumarsi A | Biol. Blood Marrow Transplant. | 2018 |
| A Qualitative Study of Chronic Pain and Self-Management in Adults with Sickle Cell Disease. | Matthie N, Ross D, Sinha C, Khemani K, Bakshi N, Krishnamurti L | J Natl Med Assoc | 2018 |
| Effects of red blood cell (RBC) transfusion on sickle cell disease recipient plasma and RBC metabolism. | Culp-Hill R, Srinivasan AJ, Gehrke S, Kamyszek R, Ansari A, Shah N, Welsby I, D'Alessandro A | Transfusion | 2018 |
| Mouse Models of Pain in Sickle Cell Disease. | Sagi V, Song-Naba WL, Benson BA, Joshi SS, Gupta K | Curr Protoc Neurosci | 2018 |
| The origin of sickle cell disease in Thailand. | Xu JZ, Riolueang S, Glomglao W, Tachavanich K, Suksangpleng T, Ekwattanakit S, Viprakasit V | Int J Lab Hematol | 2018 |
| Identification of therapeutic targets for inflammation in sickle cell disease (SCD) among Indian patients using gene expression data analysis. | Das I, Mishra H, Khodiar PK, Patra PK | Bioinformation | 2018 |
| Transfusion practices and complications in thalassemia. | Lal A, Wong TE, Andrews J, Balasa VV, Chung JH, Forester CM, Ikeda AK, Keel SB, Pagano MB, Puthenveetil G, Shah SJ, Yu JC, Vichinsky EP | Transfusion | 2018 |
| Prevalence of Sero-Molecular Markers of Hepatitis C and B Viruses among Patients with -Thalassemia Major in Northern West Bank, Palestine. | Dumaidi K, Al-Jawabreh A, Samarah F, Rabayaa M | Can J Infect Dis Med Microbiol | 2018 |
| Increased acute care utilization in a prospective cohort of adults with sickle cell disease. | Lanzkron S, Little J, Field J, Shows JR, Wang H, Seufert R, Brooks J, Varadhan R, Haywood C, Saheed M, Huang CY, Griffin B, Frymark S, Piehet A, Robertson D, Proudford M, Kincaid A, Green C, Burgess L, Wallace M, Segal J | Blood Adv | 2018 |
| A Novel β-Thalassemia Mutation in a Chinese family: IVS-II-203-205 (TCT>CC) (HBB: c.315+203TCT>CC). | Chen JK, Xin XQ, Huang JG | Hemoglobin | 2018 |
| Life-Threatening Drug-Induced Liver Injury in a Patient with β-Thalassemia Major and Severe Iron Overload on Polypharmacy. | Casale M, Picariello S, Corvino F, Cerasari G, Scianguetta S, Rossi F, Persico M, Perrotta S | Hemoglobin | 2018 |
| Targeted Hydroxyurea Education after an Emergency Department Visit Increases Hydroxyurea Use in Children with Sickle Cell Anemia. | Pecker LH, Kappa S, Greenfest A, Darbari DS, Nickel RS | J. Pediatr. | 2018 |
| Hearing loss in children with sickle cell disease: A prospective French cohort study. | Bois E, Francois M, Benkerrou M, Van Den Abbeele T, Teissier N | Pediatr Blood Cancer | 2018 |
| Transition to adult care in sickle cell disease: A longitudinal study of clinical characteristics and disease severity. | Kayle M, Docherty SL, Sloane R, Tanabe P, Maslow G, Pan W, Shah N | Pediatr Blood Cancer | 2018 |
| Reliability of the current newborn screening action value for beta thalassaemia disease detection in England: A prospective study. | Daniel Y, Henthorn J | J Med Screen | 2018 |
| Children and adolescents with sickle cell disease have worse cold and mechanical hypersensitivity during acute painful events. | Brandow AM, Hansen K, Nugent M, Pan A, Panepinto JA, Stucky CL | Pain | 2018 |
| The clinical presentation, utilization, and outcome of individuals with sickle cell anaemia presenting to urban emergency department of a tertiary hospital in Tanzania. | Sawe HR, Reynolds TA, Mfinanga JA, Runyon MS, Murray BL, Wallis LA, Makani J | BMC Hematol | 2018 |
